The Journal of International Advanced Otology
Case Report

Congenital Intratympanic Cholesteatoma in an Adult Patient: A Case Report and Review of the Literature


Department of Otolaryngology, Azienda Ospedaliera di Padova, Padova, Italy

J Int Adv Otol 2016; 12: 119-124
DOI: 10.5152/iao.2016.1807
Read: 29 Downloads: 8 Published: 03 September 2019


Congenital cholesteatoma within the tympanic membrane is an uncommon entity, with only few cases being documented. The aetiopathogenesis of this lesion is still unknown; however, when cholesteatoma develops in subjects without any history of previous ear inflammation, as in the case we report here, an embryologic origin is deeply suspected. An acquired origin is hypothesized in patients with a previous history of an inflammatory process of the external or middle ear because of the proliferation of the basal cell layer of the tympanic membrane epithelium. We report a rare case of congenital cholesteatoma of the tympanic membrane in an adult patient and review the literature.

ISSN1308-7649 EISSN 2148-3817