The Journal of International Advanced Otology
Case Report

“Emergency” Cochlear Implantation in Labyrinthitis Ossificans Secondary to Polyarteritis Nodosa: How to Face a Rare Entity

1.

Department of Otolaryngology, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy

2.

Department of Experimental Medicine, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy

3.

Department of Rheumatology, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy

J Int Adv Otol 2019; 15: 156-159
DOI: 10.5152/iao.2018.5463
Read: 231 Downloads: 23 Published: 03 September 2019

Abstract

Polyarteritis nodosa (PAN) is a systemic vasculitis affecting the small- and medium-sized arteries that may present with hearing impairment. In rare cases, PAN may be associated with progressive labyrinthitis ossificans (LO), an otologic emergency requiring early cochlear implantation (CI) to restore hearing before the complete, irreversible cochlear ossification. We report the first case in the literature of a patient affected by PAN with bilateral sudden sensorineural hearing loss and rapid LO who underwent “emergency” bilateral simultaneous CI. This case report emphasizes the importance of an early audiological evaluation in patients with PAN when LO is suspected. Multidisciplinary approach is mandatory when facing organ-specific manifestations in patients with PAN. Detailed discussion is provided with particular regard to clinical and radiological presentation as well as CI outcomes in such a rare and challenging case.

 

Cite this article as: Canzi P, Aprile F, Manfrin M, Avato I, Magnetto M, Minervini D, et al. “Emergency” Cochlear Implantation in Labyrinthitis Ossificans Secondary to Polyarteritis Nodosa: How to Face a Rare Entity. J Int Adv Otol 2019; 15(1): 156-9.

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ISSN1308-7649 EISSN 2148-3817