Original Article

Vol. 18 No. 4 (2022): The Journal of International Advanced Otology

A Unified Classification of Middle Ear and Petrous Bone Congenital Cholesteatomas

Main Article Content

Vijayendra Honnurappa
Nilesh Mahajan
Vinay Kumar Vijayendra
Miriam Redleaf

Abstract

BACKGROUND: The aim of this study was to classify congenital cholesteatoma along an entire spectrum of involvement ranging from the middle ear to petrous apex.



METHODS: A total of 131 patients (85 adults and 46 children) underwent operations for congenital cholesteatoma over the duration of 27 years.



RESULTS: For most cases, middle ear mucosa was normal, the first ossicle eroded by the mass was the stapes, and the mastoid air cell system was well-pneumatized on intraoperative and radiographic views. Totally 34% of patients presented with facial nerve weakness and 45% of these cholesteatomas arose from the supralabyrinthine area (32.8%) and from the petrous apex (12.2%).



CONCLUSION: In this unified classification system, the otologist sees congenital cholesteatoma as a continuum, with facial nerve involvement and anacusis as part of the picture. This system of congenital cholesteatoma accommodates the supralabyrinthine and petrous bone locations of the disease.



Cite this article as: Honnurappa V, Mahajan N, Kumar Vijayendra V, Redleaf M. A unified classification of middle ear and petrous bone congenital cholesteatomas. J Int Adv Otol. 2022;18(4):315-319.


Article Details